Pseudo-Exstrophy of Bladder with Unilateral Renal Agenesis: A Rare Combination of two Anomalies
Published: December 1, 2016 | DOI: https://doi.org/10.7860/JCDR/2016/20788.9082
Abdolhamid Amouei, Mohammad Baghi Yazdi, Fatemeh Ehsani, Mojtaba Babaei Zarch
1. General Surgeon, Pediateric fellowship, Surgery ward, Shahid Sadoughi University of Medical Hospital, Shahid Sadoughi, University of Medical Sciences, Yazd, Iran.
2. School of Medicine, Shahid Sadoughi University of Medical Sciences, Yazd, Iran.
3. General Surgery Resident, Surgery Ward, Shahid Sadoughi University of Medical Hospital, Shahid Sadoughi, University of Medical Sciences, Yazd, Iran.
4. School of Medicine, Shahid Sadoughi University of Medical Sciences, Yazd, Iran.
Correspondence
Dr. Mohammad Baghi Yazdi,
School of Medicine, Shahid Sadoughi university of Medical Sciences, Yazd, Iran.
Email: drbaghi7272@yahoo.com
Pseudo-exstrophy of bladder is an uncommon condition characterized by the major musculoskeletal defects without urinary system defects. A two-day-old female neonate was presented with pseudo-exstrophy of the bladder and unilateral renal agenesis- A rare combination of two anomalies. She was born at 37 weeks gestational age with caesarean section delivery. The X-ray of hip revealed pubic diastasis. Ultrasonography clearly showed absence of the left kidney with a normal right kidney. The patient was treated successfully with proper surgical management. We, hereby, report a rare variant case of pseudo-exstrophy of bladder with lower set umbilicus and infra-umbilical midline of lower anterior abdominal wall defect in a neonate who was born in Shahid Sadoughi Hospital, Yazd, Iran.
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